Aggressive juvenile fibromatosis of the paranasal sinuses: case report and brief review
Author Information
Author(s): Lakhan Shaheen E, Eager Robert M, Harle Lindsey
Primary Institution: Global Neuroscience Initiative Foundation, Los Angeles, CA, USA
Conclusion
The case reported is one of only six published accounts of pediatric desmoid fibromatosis of the paranasal sinuses, highlighting the rarity and treatment challenges of these tumors.
Supporting Evidence
- Desmoid tumors are rare, accounting for approximately 0.03% of all neoplasms.
- Individuals between the ages of 15 and 60 are most often affected; desmoid tumors are rare in the young and in the elderly.
- Histologically, desmoid tumors are characterized by small bundles of spindle cells in an abundant fibrous stroma.
Takeaway
This study talks about a rare tumor in a young boy's nose that can grow aggressively but doesn't spread to other parts of the body. Doctors usually try to remove it with surgery.
Methodology
The patient underwent functional endoscopic sinus surgery with biopsy, and histological analysis confirmed the diagnosis of extraabdominal desmoid fibromatosis.
Limitations
The rarity of the tumor limits the generalizability of the findings.
Participant Demographics
A seven-year-old male.
Digital Object Identifier (DOI)
Want to read the original?
Access the complete publication on the publisher's website