Split notochord syndrome associated with dorsal neuroenteric fistula: A rare entity
2010
Case of Split Notochord Syndrome with Dorsal Neuroenteric Fistula
Sample size: 1
publication
Evidence: low
Author Information
Author(s): Punit Srivastava, A. N. Gangopadhyay, D. K. Gupta, S. P. Sharma
Primary Institution: Department of Pediatric Surgery, IMS, BHU, Varanasi, Uttar Pradesh, India
Conclusion
The unique case of split notochord syndrome was successfully managed with a single-stage surgical procedure.
Supporting Evidence
- Only twenty cases of split notochord syndrome associated with dorsal enteric fistula have been reported in literature.
- The neonate was well managed by excision of enteric fistula and repair of associated anomalies.
- The condition is extremely rare and has not been reported earlier in this specific combination.
Takeaway
A baby was born with a rare condition where parts of his spine and intestines were not formed correctly, but doctors were able to fix it with surgery.
Methodology
The case was managed through excision of the dorsal enteric fistula, closure of the spinal defect, and repair of the hernia in a single-stage procedure.
Participant Demographics
First born, 1-day-old, male baby.
Digital Object Identifier (DOI)
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