A new 500 kb haplotype associated with high CD8+ T-lymphocyte numbers predicts a less severe expression of hereditary hemochromatosis
2008

New Genetic Markers for Hereditary Hemochromatosis

Sample size: 66 publication 10 minutes Evidence: moderate

Author Information

Author(s): Cruz Eugénia, Whittington Chris, Krikler Samuel H, Mascarenhas Cláudia, Lacerda Rosa, Vieira Jorge, Porto Graça

Primary Institution: Instituto de Biologia Molecular e Celular, Universidade do Porto, Portugal

Hypothesis

Can new genetic markers predict the clinical expression of hereditary hemochromatosis?

Conclusion

The study found that specific genetic haplotypes are associated with CD8+ T-lymphocyte numbers and the severity of hereditary hemochromatosis.

Supporting Evidence

  • A conserved haplotype was associated with low CD8+ T-lymphocyte numbers.
  • Another haplotype was linked to high CD8+ T-lymphocyte numbers and milder disease.
  • The findings were consistent across both Portuguese and Canadian patient populations.

Takeaway

Some people with a genetic condition called hereditary hemochromatosis have different levels of a type of immune cell, and this can affect how sick they get.

Methodology

Haplotype analysis was performed on genetic markers in a group of 56 Portuguese and 10 Canadian patients.

Potential Biases

Potential bias due to the selection of patients from specific geographic locations.

Limitations

The study had a small sample size and may not represent all populations.

Participant Demographics

Participants included 56 Portuguese and 10 Canadian patients, mostly Caucasian, with a mix of symptomatic and asymptomatic individuals.

Statistical Information

P-Value

p = 0.0109

Statistical Significance

p<0.05

Digital Object Identifier (DOI)

10.1186/1471-2350-9-97

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