Malignant Peripheral Nerve Sheath Tumor of the Small Bowel: A Case Report and Review of the Literature
2024

Case Report of Malignant Peripheral Nerve Sheath Tumor in the Small Bowel

Sample size: 1 publication Evidence: low

Author Information

Author(s): Muacevic Alexander, Adler John R, Ampntin Kleanthi - Christina, Tasis Nikolaos, Arnaouti Maria, Chrysi Maria, Korkolis Dimitrios P, Plastiras Aris

Primary Institution: General Anticancer and Oncology Hospital of Athens 'Saint Savvas', Athens, GRC

Conclusion

The case highlights the rarity of malignant peripheral nerve sheath tumors in the small bowel and the challenges in diagnosis and management.

Supporting Evidence

  • Malignant peripheral nerve sheath tumors are rare and account for 5%-10% of all sarcomas.
  • Less than 20 cases of intestinal MPNSTs have been recorded worldwide.
  • The patient presented with non-specific abdominal pain and vomiting.
  • Histopathological examination confirmed the diagnosis of MPNST.
  • The patient underwent successful surgical resection and had no recurrence at three months post-operation.

Takeaway

This study talks about a 78-year-old woman who had a rare tumor in her small intestine, which was hard to diagnose because it didn't show clear symptoms.

Methodology

The patient underwent exploratory laparotomy and histopathological examination for diagnosis.

Limitations

The rarity of the condition limits the generalizability of findings.

Participant Demographics

A 78-year-old woman with no history of neurofibromatosis type 1.

Digital Object Identifier (DOI)

10.7759/cureus.75189

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