Splenectomy and proximal lieno-renal shunt in a factor five deficient patient with extra-hepatic portal vein obstruction
2006

Surgery for Factor V Deficiency and Portal Vein Obstruction

Sample size: 1 publication Evidence: low

Author Information

Author(s): Chava Srinivas Prabhu, Pal Sujoy, Ghatak Supriyo, Kumar Rajat, Sahni Peush, Chattopadhyay Tushar Kanti

Primary Institution: All India Institute of Medical Sciences, New Delhi, India

Hypothesis

Can surgical portal decompression be safely performed in patients with factor V deficiency and portal hypertension?

Conclusion

Surgical procedures can be safely performed in patients with factor V deficiency if proper hemostasis and factor replacement are managed.

Supporting Evidence

  • The patient had a history of recurrent upper gastrointestinal bleeding.
  • Surgery was performed without excessive bleeding.
  • The patient received fresh frozen plasma before and after surgery.

Takeaway

A boy with a rare blood condition had successful surgery to fix his bleeding problem, and he is doing well now.

Methodology

The patient underwent splenectomy and proximal lieno-renal shunt with fresh frozen plasma transfusions.

Limitations

The study is based on a single case, limiting generalizability.

Participant Demographics

A 16-year-old boy with factor V deficiency.

Digital Object Identifier (DOI)

10.1186/1471-2482-6-7

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