Takayasu arteritis presenting as cerebral aneurysms in an 18 month old: A case report
2008

Takayasu Arteritis in an 18-Month-Old Girl with Cerebral Aneurysms

Sample size: 1 publication Evidence: low

Author Information

Author(s): Pamela F Weiss, Diana A Corao, Avrum N Pollock, Terri H Finkel, Sabrina E Smith

Primary Institution: The Children's Hospital of Philadelphia, University of Pennsylvania School of Medicine

Hypothesis

Should all patients with cerebral aneurysms be evaluated for systemic aneurysms and/or vasculitis?

Conclusion

This case highlights cerebral aneurysm as a highly unusual initial manifestation of Takayasu arteritis in a child.

Supporting Evidence

  • Central nervous system involvement occurs in as many as twenty percent of Takayasu arteritis cases.
  • This case demonstrates that Takayasu arteritis can cause cerebral aneurysms in children.
  • Diagnosis of Takayasu arteritis is challenging in the early inflammatory phase.

Takeaway

A young girl had a rare condition called Takayasu arteritis that caused her to develop brain aneurysms, which is not common in children.

Methodology

Case report detailing clinical presentation, imaging studies, and pathological findings.

Limitations

The diagnosis of Takayasu arteritis was not considered until late in the clinical course.

Participant Demographics

An 18-month-old Caucasian girl.

Digital Object Identifier (DOI)

10.1186/1546-0096-6-4

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