Kbus/Idr, a mutant mouse strain with skeletal abnormalities and hypophosphatemia: Identification as an allele of 'Hyp'
2011

Kbus/Idr Mouse Strain: A New Model for Studying Bone and Phosphate Disorders

Sample size: 5 publication Evidence: moderate

Author Information

Author(s): Moriyama Kenji, Hanai Atsuko, Mekada Kazuyuki, Yoshiki Atsushi, Ogiwara Katsueki, Kimura Atsushi, Takahashi Takayuki

Primary Institution: Mukogawa Women's University

Hypothesis

The Kbus/Idr mouse strain carries a novel mutation in the Phex gene that leads to skeletal abnormalities and hypophosphatemia.

Conclusion

The Kbus mouse model is a valuable tool for understanding the mechanisms of bone mineralization and phosphate homeostasis.

Supporting Evidence

  • Kbus/Idr mice exhibited bone mineralization defects inherited in an X chromosome-linked dominant manner.
  • RT-PCR experiments identified a novel mutation in the Phex gene associated with hypophosphatemic rickets.
  • Alkaline phosphatase activity was significantly higher in Kbus/Idr mice compared to control mice.

Takeaway

Scientists created a special mouse that has bone problems and low phosphate levels, which helps them learn more about similar issues in humans.

Methodology

Histopathological and X-ray examinations, RT-PCR, and biochemical assays were performed to characterize the Kbus/Idr mouse strain.

Limitations

The study primarily focused on skeletal abnormalities without exploring other potential health impacts of the mutation.

Participant Demographics

Mice were highly inbred Kbus/Idr strains maintained for over 20 generations.

Statistical Information

P-Value

p<0.01

Statistical Significance

p<0.01

Digital Object Identifier (DOI)

10.1186/1423-0127-18-60

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