Congenital pulmonary lymphangiectasia
2006

Congenital Pulmonary Lymphangiectasia

publication Evidence: moderate

Author Information

Author(s): Carlo Bellini, Francesco Boccardo, Corradino Campisi, Eugenio Bonioli

Primary Institution: University of Genoa, G. Gaslini Institute, Genoa, Italy

Conclusion

Recent advances in intensive neonatal care have improved the previously high mortality rate associated with congenital pulmonary lymphangiectasia at birth.

Supporting Evidence

  • Congenital pulmonary lymphangiectasia presents at birth with severe respiratory distress and has a high mortality rate.
  • Most reported cases of congenital pulmonary lymphangiectasia are sporadic and the etiology is not completely understood.
  • Recent advances in neonatal care have changed the previously nearly fatal outcome of congenital pulmonary lymphangiectasia.

Takeaway

Congenital pulmonary lymphangiectasia is a rare lung condition that can cause serious breathing problems in newborns, but better medical care has helped many survive.

Methodology

The study reviews the clinical presentation, diagnostic methods, and management of congenital pulmonary lymphangiectasia.

Limitations

The incidence and prevalence of congenital pulmonary lymphangiectasia are not well defined due to the rarity of cases.

Digital Object Identifier (DOI)

10.1186/1750-1172-1-43

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