Ehlers-Danlos syndrome type IV
2007

Ehlers-Danlos Syndrome Type IV Overview

publication Evidence: high

Author Information

Author(s): Dominique P Germain

Primary Institution: Assistance Publique – Hôpitaux de Paris, Paris, France

Conclusion

Ehlers-Danlos syndrome type IV is a serious inherited connective tissue disorder that leads to severe vascular and digestive complications.

Supporting Evidence

  • Ehlers-Danlos syndrome type IV is characterized by severe arterial and digestive complications.
  • Patients with EDS type IV are at high risk for vascular ruptures and digestive perforations.
  • The median age of death for individuals with EDS type IV is estimated to be 50 years.

Takeaway

Ehlers-Danlos syndrome type IV is a condition that makes your blood vessels and digestive system very fragile, which can cause serious problems like tears and ruptures.

Digital Object Identifier (DOI)

10.1186/1750-1172-2-32

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