Assessing Behavioural Manifestations Prior to Clinical Diagnosis of Huntington Disease: 'Anger and Irritability' and 'Obsessions and Compulsions'
2011

Assessing Behavioral Symptoms in Huntington Disease

Sample size: 225 publication Evidence: moderate

Author Information

Author(s): Anthony L Vaccarino, Karen E. Anderson, Beth Borowsky, Emil Craufurd, Jean Endicott, Joseph Giuliano, Mark Groves, Mark Guttman, Aileen K Ho, Peter Kupchak, Jane S. Paulsen, Matthew S. Stanford, Daniel P van Kammen, David Watson, Kevin D Wu, Ken Evans

Primary Institution: Ontario Cancer Biomarker Network

Hypothesis

Can we develop a valid scale to assess early behavioral symptoms in Huntington disease gene expansion carriers?

Conclusion

The study successfully developed and beta tested interview questions for assessing 'Anger and Irritability' and 'Obsessions and Compulsions' in individuals at risk for Huntington disease.

Supporting Evidence

  • The study involved input from patients, caregivers, and experts to develop relevant interview questions.
  • Field testing was conducted with a target sample size of 100 participants.
  • Six interview questions were identified for further testing based on their scoring and discrimination properties.

Takeaway

Researchers are trying to find out how people with a gene for Huntington disease feel before they get sick, focusing on anger and obsessive thoughts.

Methodology

The study involved developing interview questions through input from experts and field testing them with individuals at risk for Huntington disease.

Potential Biases

Potential bias from self-reported symptoms and the small sample size for some questions.

Limitations

Some symptoms were rarely endorsed, limiting their usefulness for assessment.

Participant Demographics

{"total":225,"prHD":190,"HD":35,"male_percentage":44,"age_range":"18-81"}

Statistical Information

P-Value

0.81

Statistical Significance

p = 0.81

Digital Object Identifier (DOI)

10.1371/currents.RRN1241

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