Reverse Phenotyping: Addressing Refractory Seizures From an Endocrine Perspective
2024

Addressing Refractory Seizures from an Endocrine Perspective

Sample size: 1 publication Evidence: low

Author Information

Author(s): Muacevic Alexander, Adler John R, Sherin Shijiya, Soodhana Dhanya, Mohanlal Smilu, Pachat Divya

Primary Institution: Aster Malabar Institute of Medical Sciences, Kozhikode, IND

Hypothesis

Can metabolic etiologies like hyperinsulinemic hypoglycemia be considered in children with seizures resistant to standard antiepileptic drugs?

Conclusion

The case highlights the importance of early recognition and targeted therapy for achieving seizure control in children with refractory seizures.

Supporting Evidence

  • The child had a heterozygous pathogenic mutation in the GLUD1 gene.
  • Treatment with diazoxide improved blood sugar levels and seizure control.
  • Seizures were initially resistant to standard antiepileptic medications.

Takeaway

A 2-year-old girl with seizures was found to have a genetic condition causing low blood sugar, and treatment helped her stop having seizures.

Methodology

The case involved genetic testing and treatment with diazoxide after identifying a mutation in the GLUD1 gene.

Limitations

The study is based on a single case, which may limit the generalizability of the findings.

Participant Demographics

A 2-year-old girl, born to non-consanguineous parents.

Digital Object Identifier (DOI)

10.7759/cureus.75146

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