Ataxia telangiectasia genes and predisposition to leukaemia, lymphoma and breast cancer
1992

Genetic Links Between Ataxia Telangiectasia and Cancer

Sample size: 10 Editorial Evidence: moderate

Author Information

Author(s): A.M.R. Taylor

Primary Institution: University of Birmingham

Hypothesis

Is there familial predisposition to leukaemia associated with ataxia telangiectasia?

Conclusion

Ataxia telangiectasia significantly increases the risk of lymphocytic leukaemia and lymphoma.

Supporting Evidence

  • About 10% of all ataxia telangiectasia homozygotes develop a malignancy in childhood or early childhood.
  • Patients with ataxia telangiectasia show a 70-fold excess for leukaemias and a 250-fold excess for lymphomas.
  • Carriers of the ataxia telangiectasia gene have a cancer risk that is two to six times higher than the normal population.

Takeaway

Some people with a condition called ataxia telangiectasia are more likely to get certain types of blood cancer.

Methodology

The study involved visiting 60 families with ataxia telangiectasia and documenting cases of leukaemia/lymphoma.

Limitations

The study is based on a small number of cases, which may not represent the broader population.

Participant Demographics

The study included 8 cases of leukaemia/lymphoma from families with ataxia telangiectasia, with a mix of male and female patients.

Want to read the original?

Access the complete publication on the publisher's website

View Original Publication