Early stage transplantation of bone marrow cells markedly ameliorates copper metabolism and restores liver function in a mouse model of Wilson disease
2011

Bone Marrow Cell Transplantation Improves Liver Function in Wilson Disease Mice

Sample size: 240 publication 10 minutes Evidence: moderate

Author Information

Author(s): Chen Xi, Xing Shihui, Feng Yanqing, Chen Songlin, Pei Zhong, Wang Chuhuai, Liang Xiuling

Primary Institution: The First Affiliated Hospital, Sun Yat-Sen University

Hypothesis

The study investigates the impact of normal bone marrow cell transplantation at different stages of Wilson disease on liver injury correction.

Conclusion

Early stage transplantation of normal bone marrow cells is more effective than late stage transplantation in improving liver function and copper metabolism in a mouse model of Wilson disease.

Supporting Evidence

  • Bone marrow cells transplantation at 2 months significantly corrected liver function and copper levels.
  • Transplantation at 5 months showed limited improvement in liver function.
  • The study used a well-defined mouse model of Wilson disease.

Takeaway

Transplanting bone marrow cells early helps fix liver problems in mice with Wilson disease better than doing it later.

Methodology

Mice were irradiated and received bone marrow cell transplants at different ages, with evaluations of liver function and copper levels over time.

Limitations

The study was conducted in a mouse model, which may not fully replicate human Wilson disease.

Participant Demographics

Tx mice, genetically modified to model Wilson disease, were used in the study.

Statistical Information

P-Value

p<0.05

Statistical Significance

p<0.05

Digital Object Identifier (DOI)

10.1186/1471-230X-11-75

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