Dysregulated brain creatine kinase is associated with hearing impairment in mouse models of Huntington disease
2011

The Role of Brain-Type Creatine Kinase in Hearing Impairment

publication Evidence: moderate

Author Information

Author(s): Lin Yow-Sien, Wang Chih-Hung, Chern Yijuang

Primary Institution: National Yang-Ming University

Hypothesis

Does brain-type creatine kinase play a role in hearing impairment from common pathological causes?

Conclusion

Dietary creatine supplementation may improve hearing loss associated with Huntington's disease and other forms of hearing impairment.

Supporting Evidence

  • Patients and mice with Huntington's disease show hearing impairment linked to brain-type creatine kinase.
  • Dietary creatine supplementation improved hearing in HD mice.
  • Impaired energy homeostasis is a significant factor in neurodegenerative diseases.

Takeaway

This study suggests that a substance called creatine might help people with hearing problems, especially those with Huntington's disease.

Methodology

The study involved examining the expression of brain-type creatine kinase in cochlear tissues of mouse models and assessing the effects of dietary creatine supplementation.

Limitations

The study primarily focuses on mouse models, which may not fully represent human conditions.

Digital Object Identifier (DOI)

10.1172/JCI45912

Want to read the original?

Access the complete publication on the publisher's website

View Original Publication