Rosai-Dorfman Disease: A previously unreported association with Sickle Cell Disease
2007

Rosai-Dorfman Disease and Sickle Cell Disease in a Child

Sample size: 1 publication Evidence: low

Author Information

Author(s): Claire Stebbing, Jon van der Walt, Ghada Ramadan, Baba Inusa

Primary Institution: Guy's and St Thomas' Hospital, London, UK

Conclusion

This case presents the first documented occurrence of Rosai-Dorfman Disease in a child with Sickle Cell Disease.

Supporting Evidence

  • The child was diagnosed with Sickle Cell Anemia at birth.
  • Massive lymphadenopathy was noted during routine check-ups.
  • A biopsy confirmed the diagnosis of Rosai-Dorfman Disease.
  • The child experienced complications from Sickle Cell Disease, including cardiomyopathy.

Takeaway

A boy with Sickle Cell Disease also had a rare condition called Rosai-Dorfman Disease, which caused swollen lymph nodes.

Methodology

Case report detailing the medical history and clinical findings of a child diagnosed with both diseases.

Limitations

The case is based on a single patient, limiting generalizability.

Participant Demographics

A three-year-old Nigerian boy.

Digital Object Identifier (DOI)

10.1186/1472-6890-7-3

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