Atlanto-axial rotatory fixation in a girl with Spondylocarpotarsal synostosis syndrome
2006

Case Report of Atlanto-axial Rotatory Fixation in a Girl with Spondylocarpotarsal Synostosis Syndrome

Sample size: 1 publication Evidence: low

Author Information

Author(s): Ali Al Kaissi, Farid Ben Chehida, Hassan Gharbi, Maher Ben Ghachem, Franz Grill, Klaus Klaushofer

Primary Institution: Ludwig-Boltzmann Institute of Osteology at the Hanusch Hospital of WGKK and AUVA Trauma Centre Meidling

Hypothesis

The study investigates the association of atlanto-axial rotatory fixation with spondylocarpotarsal synostosis syndrome in a pediatric patient.

Conclusion

This case report highlights the importance of CT scans in diagnosing craniocervical malformations in patients with spondylocarpotarsal synostosis syndrome.

Supporting Evidence

  • The patient presented with spinal malsegmentation and other skeletal anomalies.
  • CT scans were crucial in identifying the craniocervical malformation.
  • This is the first clinical report linking atlanto-axial rotatory fixation with spondylocarpotarsal synostosis syndrome.

Takeaway

A 15-year-old girl had a rare condition where her neck bones were stuck in a twisted position, and doctors used special scans to understand her problem better.

Methodology

The study involved clinical evaluation, radiographic analysis, and CT scans to assess the patient's condition.

Limitations

The study is based on a single case report, limiting the generalizability of the findings.

Participant Demographics

The participant was a 15-year-old girl with a family history of genetic disorders.

Digital Object Identifier (DOI)

10.1186/1748-7161-1-15

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