Case Report on OHVIRA Syndrome in a Young Girl
Author Information
Author(s): Telecan Teodora, Capras Roxana Denisa, Filip Gabriela Adriana, Ionutas Emanuela Maria, Stanca Dan Vasile, Crivii Carmen-Bianca
Primary Institution: Department of Anatomy and Embryology, “Iuliu Hatieganu” University of Medicine and Pharmacy, Cluj-Napoca, Romania
Conclusion
The case highlights the rarity of OHVIRA syndrome diagnosed in prepubertal girls and the importance of multidisciplinary management.
Supporting Evidence
- OHVIRA syndrome occurs in 5.5% of female newborns and is characterized by complex malformations.
- The patient was diagnosed with ipsilateral renal hypoplasia and ectopic ureteral implantation.
- Total nephrectomy was performed due to urinary incontinence after the vaginal septum incision.
- This is the first reported case of OHVIRA syndrome with ectopic ureter draining at the level of the ipsilateral hemiuterus.
Takeaway
This study is about a 7-year-old girl who had a rare condition called OHVIRA syndrome, which affected her kidneys and urinary system. After surgery, she no longer had problems with incontinence.
Methodology
The patient underwent imaging studies, a retrograde urethrocystoscopy, and a 3D laparoscopic total nephrectomy.
Limitations
The study is based on a single case report, limiting the generalizability of the findings.
Participant Demographics
A 7-year-old asymptomatic premenarchal female patient.
Digital Object Identifier (DOI)
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