Recurrent retroperitoneal hemorrhage in a patient with tuberous sclerosis complex: a case report
2008

Recurrent Retroperitoneal Hemorrhage in a Patient with Tuberous Sclerosis Complex

Sample size: 1 publication Evidence: low

Author Information

Author(s): Chiarugi Massimo, Martino Maria Carola, Pucciarelli Marsia, Decanini Luigi, Vignali Claudio

Primary Institution: University of Pisa

Conclusion

Transarterial embolization is effective in preventing and controlling hemorrhage in patients with AMLs of the kidney.

Supporting Evidence

  • Angiomyolipomas (AML) are the most common TSC lesion, occurring in 70 to 80% of adults and older children.
  • Bleeding from ruptured aneurysm increases in frequency when tumors become larger than 4 cm.
  • Transarterial embolization is proposed as the first choice of intervention for symptomatic AMLs.

Takeaway

A patient with a genetic condition had serious bleeding from kidney tumors, but doctors were able to stop the bleeding with a special procedure.

Methodology

The patient underwent angiography and selective embolization to manage the bleeding.

Limitations

The patient developed mild renal failure after treatment.

Participant Demographics

48 year-old Caucasian male with sporadic tuberous sclerosis.

Digital Object Identifier (DOI)

10.1186/1757-1626-1-424

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