Malformations in Adults with Polysplenia on CT: A Pilot Study
Author Information
Author(s): Gu Xinru, Xu Shuangshuang, Chen Jinghua, Jiang Xiaoqin, Xie Ping, Fang Xiang, Gao Yan, Huang Jian, Liu Kefu
Primary Institution: The Affiliated Suzhou Hospital of Nanjing Medical University, Suzhou, Jiangsu, China
Hypothesis
To analytically depict the associated malformations of polysplenia syndrome (PS) in adults via computed tomography (CT).
Conclusion
PS is a complex malformation syndrome involving multiple systems, with the most common malformation being a short pancreas.
Supporting Evidence
- 75% of patients presented with left lung heterogeneity.
- 100% of patients had a short pancreas.
- 67% of patients exhibited midgut malrotation.
- 75% of patients had hepatic segmental IVC agenesis with continuation of the azygos vein.
Takeaway
This study looked at adults with a rare condition called polysplenia syndrome, which means they have extra spleens and other body parts that are not in the usual places. The researchers used special scans to see what other problems these patients might have.
Methodology
The incidence of malformations associated with PS in twelve adult patients was retrospectively analyzed via CT imaging.
Limitations
The study is retrospective and based on a small sample size.
Participant Demographics
5 men and 7 women, aged 30–74 years.
Digital Object Identifier (DOI)
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