The Tissue-Specific Rep8/UBXD6 Tethers p97 to the Endoplasmic Reticulum Membrane for Degradation of Misfolded Proteins Rep8 Is a Tissue-Specific p97 Cofactor
2011

Rep8: A Tissue-Specific Cofactor for p97 in Protein Degradation

publication 10 minutes Evidence: moderate

Author Information

Author(s): Madsen Louise, Kriegenburg Franziska, Vala Andrea, Best Diana, Prag Søren, Hofmann Kay, Seeger Michael, Adams Ian R., Hartmann-Petersen Rasmus

Primary Institution: Department of Biology, University of Copenhagen, Copenhagen, Denmark

Hypothesis

Rep8 is a tissue-specific cofactor for the p97 ATPase involved in the degradation of misfolded proteins.

Conclusion

Rep8 tethers p97 to the ER membrane, facilitating the degradation of misfolded proteins.

Supporting Evidence

  • Rep8 is highly tissue-specific and abundant in gonads.
  • Knock-down of Rep8 expression leads to decreased p97 association with the ER membrane.
  • Rep8 interacts directly with p97 via its UBX domain.
  • Rep8 is a transmembrane protein localized to the ER membrane.
  • Rep8 expression is primarily found in testes and ovaries.

Takeaway

Rep8 helps a protein called p97 do its job of getting rid of bad proteins in certain tissues, like the testis and ovary.

Methodology

The study involved yeast two-hybrid screening, co-precipitation experiments, and differential centrifugation to analyze the interaction and localization of Rep8 and p97.

Limitations

The study primarily focuses on the interaction in cell lines and may not fully represent in vivo conditions.

Participant Demographics

The study involved human cell lines and rat tissues.

Statistical Information

P-Value

p<0.01

Statistical Significance

p<0.01

Digital Object Identifier (DOI)

10.1371/journal.pone.0025061

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