Fluctuating Hemiparesis Secondary to Moyamoya Phenomenon in a Child with Down Syndrome: a case report
2008

Fluctuating Hemiparesis in a Child with Down Syndrome

Sample size: 1 publication Evidence: low

Author Information

Author(s): Rison Richard A

Primary Institution: University of Southern California, Keck School of Medicine

Hypothesis

The study investigates the association between moyamoya phenomenon and Down syndrome in a pediatric patient.

Conclusion

Surgical revascularization with encephalomyosynangiosis may confer long-term benefits for patients with Down syndrome and moyamoya phenomenon.

Supporting Evidence

  • The patient presented with fluctuating right-sided weakness and facial droop.
  • Characteristic 'puff of smoke' patterns were observed on angiographic studies.
  • The association of moyamoya with Down syndrome is not fully understood.

Takeaway

This study talks about a young girl with Down syndrome who had weakness on one side of her body due to a condition called moyamoya, and she got better after surgery.

Methodology

The patient was treated with aspirin and underwent an encephalomyosynangiosis after presenting with fluctuating weakness.

Limitations

The patient was lost to follow-up after initial satisfactory outcomes.

Participant Demographics

A 4.5-year-old Mexican girl with Down syndrome.

Digital Object Identifier (DOI)

10.1186/1757-1626-1-240

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