Identification of a Heritable Polymorphism in Bovine PRNP Associated with Genetic Transmissible Spongiform Encephalopathy: Evidence of Heritable BSE
2008

Heritable Polymorphism in Bovine PRNP Linked to BSE

Sample size: 2 publication Evidence: moderate

Author Information

Author(s): Eric M. Nicholson, Brian W. Brunelle, Juergen A. Richt, Marcus E. Kehrli Jr, Justin J. Greenlee

Primary Institution: National Animal Disease Center, USDA, Agricultural Research Service, Ames, Iowa, USA

Hypothesis

Is the E211K polymorphism in the bovine prion gene a heritable trait associated with BSE?

Conclusion

The E211K polymorphism is a heritable trait in cattle, suggesting that BSE may be transmitted genetically.

Supporting Evidence

  • Both the 2006 US atypical BSE animal and its offspring were found to carry the E211K polymorphism.
  • The E211K polymorphism is analogous to a human genetic TSE mutation.
  • This study is the first to provide evidence of a heritable form of BSE in cattle.

Takeaway

Scientists found a change in a gene in cows that could be passed down, which might mean BSE can be inherited, not just caught from food.

Methodology

DNA from a 2-year-old heifer and a BSE-positive animal was sequenced to analyze the prion gene.

Limitations

No parental information for the BSE case limits understanding of the polymorphism's inheritance.

Participant Demographics

The study involved a 2-year-old heifer and its BSE-positive parent.

Digital Object Identifier (DOI)

10.1371/journal.pone.0002912

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