Ocular modifications in a young girl with cryopyrin-associated periodic syndromes responding to interleukin-1 receptor antagonist anakinra
2011

Ocular Changes in a Young Girl with CAPS Treated with Anakinra

Sample size: 1 publication Evidence: low

Author Information

Author(s): Terrada Celine, Neven Benedicte, Boddaert Nathalie, Souied Eric H, Prieur Anne Marie, Quartier Pierre, Lehoang Phuc, Bodaghi Bahram

Primary Institution: Department of Ophthalmology, APHP, Pitie-Salpetriere Hospital, Paris, France

Hypothesis

Can interleukin-1 receptor antagonist anakinra effectively treat ocular symptoms in a young girl with cryopyrin-associated periodic syndromes?

Conclusion

The treatment with anakinra led to the resolution of all symptoms and normalization of ophthalmologic signs in the patient.

Supporting Evidence

  • The patient had recurrent episodes of fever, rash, and ocular involvement before treatment.
  • All symptoms related to the disease ceased within a few days of starting anakinra.
  • Biologic inflammatory markers normalized after one month of treatment.

Takeaway

A young girl with a rare syndrome had her eye problems go away after taking a special medicine called anakinra.

Methodology

The patient was treated with anakinra, and her symptoms and inflammation were monitored over a follow-up period of 30 months.

Limitations

The study is based on a single case report, limiting generalizability.

Participant Demographics

An 8-year-old Caucasian girl.

Digital Object Identifier (DOI)

10.1007/s12348-010-0018-2

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