Methionine Sulfoxides on Prion Protein Helix-3 Switch on the α-Fold Destabilization Required for Conversion PrP Methionine Oxidation
2009

Methionine Oxidation and Prion Protein Stability

publication Evidence: moderate

Author Information

Author(s): Colombo Giorgio, Meli Massimiliano, Morra Giulia, Gabizon Ruth, Gasset María

Primary Institution: Isto di Chimica del Riconoscimento Molecolare, Consiglio Nazionale delle Ricerche, Milano, Italy

Hypothesis

Does methionine oxidation play a role in the misfolding process of prion proteins?

Conclusion

The sulfoxidation of Helix-3 methionines destabilizes the prion protein's α-fold, potentially triggering its conversion to a pathogenic form.

Supporting Evidence

  • The oxidation of methionine residues alters the dynamics and stability of the prion protein.
  • Oxidation increases the flexibility of the protein, favoring alternative states.
  • Sulfoxidation of methionines is a covalent signature for the infectious form of prion proteins.
  • Changes in protein dynamics may facilitate the conversion to a pathogenic form.

Takeaway

When certain parts of a protein called methionines get oxidized, it makes the protein less stable and more likely to change into a harmful form.

Methodology

Molecular dynamics simulations were used to study the effects of methionine oxidation on the stability and dynamics of the prion protein.

Limitations

The study's results are qualitative due to limitations in the time-scales simulated at room temperature.

Digital Object Identifier (DOI)

10.1371/journal.pone.0004296

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