Electrical storm in a patient with Charcot–Marie–Tooth disease treated with radiofrequency ablation and subsequent serious complication of implantable cardioverter defibrillator implantation: a case report
2024

Electrical Storm in a Patient with Charcot–Marie–Tooth Disease

Sample size: 1 publication Evidence: low

Author Information

Author(s): Jiří Vrtal, Jiří Plášek, Jan Václavík, David Šipula, Jozef Dodulík

Primary Institution: University Hospital Ostrava, University of Ostrava

Hypothesis

How can we effectively manage electrical storms in patients with Charcot–Marie–Tooth disease?

Conclusion

The patient successfully underwent radiofrequency ablation for electrical storm but experienced a serious complication during ICD implantation.

Supporting Evidence

  • The patient had a history of Type 1A Charcot–Marie–Tooth disease.
  • Radiofrequency ablation was performed due to ineffective conservative therapy.
  • The patient experienced lead perforation after ICD implantation.

Takeaway

A 69-year-old man with a rare nerve disease had a heart problem that needed special treatment, but he faced complications from the device that helps his heart.

Methodology

The patient underwent radiofrequency ablation followed by ICD implantation, with monitoring and follow-up assessments.

Potential Biases

Potential bias in decision-making due to the rarity of the condition and lack of established guidelines.

Limitations

The case is based on a single patient, limiting the generalizability of the findings.

Participant Demographics

69-year-old male with Type 1A Charcot–Marie–Tooth disease.

Digital Object Identifier (DOI)

10.1093/ehjcr/ytae673

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