A Micro RNA Processing Defect in Rapidly Progressing Idiopathic Pulmonary Fibrosis
2011

MicroRNA Processing Defect in Rapidly Progressing Idiopathic Pulmonary Fibrosis

Sample size: 25 publication 10 minutes Evidence: moderate

Author Information

Author(s): Sameer R. Oak, Lynne Murray, Athula Herath, Matthew Sleeman, Ian Anderson, Amrita D. Joshi, Ana Lucia Coelho, Kevin R. Flaherty, Galen B. Toews, Darryl Knight, Fernando J. Martinez, Cory M. Hogaboam

Primary Institution: University of Michigan Medical School

Hypothesis

Differential miRNA expression might provide one explanation for rapidly versus slowly progressing forms of IPF.

Conclusion

The development and/or clinical progression of IPF might be the consequence of aberrant miRNA processing.

Supporting Evidence

  • 11 miRNAs were significantly increased and 36 were significantly decreased in rapid biopsies compared with normal biopsies.
  • 5 miRNAs were significantly increased in rapid compared with slow IPF lung biopsies.
  • AGO1 and AGO2 expression were lower in rapidly progressive IPF biopsies compared to normal and slowly progressive biopsies.

Takeaway

This study found that certain tiny molecules in the lungs, called microRNAs, are different in patients with fast and slow forms of a lung disease called idiopathic pulmonary fibrosis.

Methodology

miRNA and mRNA were isolated from lung biopsies of IPF patients and analyzed using a quantitative PCR miRNA array.

Potential Biases

Potential bias in patient selection and classification of disease progression.

Limitations

The study is limited by the small sample size and the retrospective grouping of patients.

Participant Demographics

9 rapidly progressive IPF patients (7 male, 2 female, median age 66) and 6 slowly progressive IPF patients (2 male, 4 female, median age 61).

Statistical Information

P-Value

0.0003 to 0.00003 for various miRNAs

Statistical Significance

p<0.05

Digital Object Identifier (DOI)

10.1371/journal.pone.0021253

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