Evaluation of SHOX copy number variations in patients with Müllerian aplasia
2011

Study of SHOX Variations in Müllerian Aplasia Patients

Sample size: 216 publication Evidence: moderate

Author Information

Author(s): Maria Sandbacka, Mervi Halttunen, Varpu Jokimaa, Kristiina Aittomäki, Hannele Laivuori

Primary Institution: Folkhälsan Institute of Genetics, Helsinki, Finland

Hypothesis

Does SHOX copy number variation contribute to Müllerian aplasia?

Conclusion

The study found no evidence supporting a role for SHOX copy number variations in Müllerian aplasia.

Supporting Evidence

  • All patients showed normal amplification of SHOX.
  • Several aberrations were found downstream of the gene in five patients and seven controls, but these were all copy number polymorphisms.
  • The study suggests that SHOX duplications are not a major cause of Müllerian aplasia.

Takeaway

The researchers looked at a gene called SHOX in women with a condition that affects their reproductive organs, but they didn't find any problems with this gene that could explain the condition.

Methodology

Multiplex ligation-dependent probe amplification (MLPA) was used to study SHOX copy number variations.

Limitations

The study did not find any causative SHOX aberrations, suggesting that other genetic factors may be involved in Müllerian aplasia.

Participant Demographics

101 Finnish patients with Müllerian aplasia and 115 healthy female controls.

Digital Object Identifier (DOI)

10.1186/1750-1172-6-53

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