Imprinted CDKN1C Is a Tumor Suppressor in Rhabdoid Tumor and Activated by Restoration of SMARCB1 and Histone Deacetylase Inhibitors
2009

CDKN1C as a Tumor Suppressor in Rhabdoid Tumor

publication Evidence: moderate

Author Information

Author(s): Algar Elizabeth M., Muscat Andrea, Dagar Vinod, Rickert Christian, Chow C. W., Biegel Jaclyn A., Ekert Paul G., Saffery Richard, Craig Jeff, Johnstone Ricky W., Ashley David M.

Primary Institution: Children's Cancer Centre research laboratory, Murdoch Children's Research Institute, Royal Children's Hospital, Parkville, Australia

Hypothesis

The oncogenic pathway in rhabdoid tumors involves epigenetic silencing of key cell cycle regulators due to loss of SMARCB1.

Conclusion

CDKN1C expression is critical for preventing rhabdoid tumor growth, and its restoration through histone deacetylase inhibitors may offer therapeutic potential.

Supporting Evidence

  • CDKN1C expression induces cell cycle arrest in rhabdoid tumor cells.
  • Restoration of CDKN1C expression through histone deacetylase inhibitors leads to reduced tumor cell proliferation.
  • CDKN1C is commonly silenced in clinical specimens of rhabdoid tumors.

Takeaway

This study found that a gene called CDKN1C helps stop cancer cells from growing, and when it's turned off in a type of cancer called rhabdoid tumor, the cancer can grow faster.

Methodology

The study used an inducible expression system to analyze the effects of CDKN1C and SMARCB1 on cell cycle regulation in rhabdoid tumor cell lines.

Limitations

The study primarily focused on cell lines and clinical specimens, which may not fully represent the complexity of rhabdoid tumors in patients.

Digital Object Identifier (DOI)

10.1371/journal.pone.0004482

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